Table 2, online only.
Initial and subsequent surgical procedures in patients with Trisomy 21a
| Procedure Name N (%) | Initial procedure (n = 3,571) | Procedure Name N (%) | Subsequent procedure (n =852) |
|---|---|---|---|
| CAVC repair | 1,445 (40.4) | LAVV repair or replacement | 188 (22.1) |
| VSD closure | 948 (26.6) | Permanent pacemaker | |
| initial | 115 (13.5) | ||
| replacement | 52 (6.1) | ||
| Incomplete AVC repair | 319 (8.9) | CAVC repair | 126 (14.8) |
| ASD repair | 238 (6.7) | VSD closure | 74 (8.7) |
| TOF repair | 152 (4.3) | Subaortic resection | 58 (6.8) |
| PA band | 135 (3.8) | TOF repair | 54 (6.3) |
| AP shunt | 132 (3.7) | TOF + CAVC repair | 39 (4.6) |
| TOF + CAVC repair | 75 (2.1) | AP shunt | 26 (3.0) |
| CoA/IAA repair | 54 (1.6) | RVOT procedure | 17 (2.0) |
| PDA ligation | 43 (1.2) | Supravalvar aortic stenosis repair | 14 (1.6) |
| Other1 | 30 (1.0) | Other2 | 89 (10.5) |
Given are frequency (n) and percent (%).
Note that diagnoses and procedures do not match completely; some patients underwent palliative procedures or reoperations.
CAVC = common atrioventricular canal; VSD = ventricular septal defect; Incomplete AVC = incomplete atrioventricular canal (partial and transitional); ASD = atrial septal defect; TOF = tetralogy of Fallot; PA = pulmonary artery; AP = aortopulmonary; CoA = coarctation of the aorta; IAA = interrupted aortic arch; PDA = patent ductus arteriosus; LAVV = left atrioventricular valve; RVOT = right ventricular outflow tract.
Other includes left ventricle to aorta tunnel (n= 13), CAVC + CoA (n = 8), RVOT procedure (n = 7), left atrioventricular (mitral) valve repair/replacement (n = 2).
Other2 includes right atrioventricular valve repair/replacement (n = 13), pulmonary valve replacement n= 12, ASD repair (n = 11), PA band (n = 10), pulmonary arterioplasty (n = 10), PDA ligation (n= 8), incomplete AVC repair (n= 7), CoA/IAA repair (n = 5), extracorporeal life support (n = 4), subpulmonary stenosis repair (n = 4), left ventricle to aorta tunnel (n = 2), atrial mass resection (n= 2) CAVC + CoA repair (n = 1).