Table 1.
Patient characteristics
| Demographics | |
| Number | 57 |
| Age (y) | 34 (26–47) |
| Female | 48/9 |
| Disease duration (months) | 3 (1–12) |
| Clinical features | |
| Fever > 39 °C | 46 (80.7) |
| Skin rash | 52 (91.2) |
| Arthralgia | 52 (91.2) |
| Sore throat | 44 (77.2) |
| Lymphadenopathy | 43 (75.4) |
| Splenomegaly | 25 (43.9) |
| Hepatomegaly | 9 (15.8) |
| Pleuritis | 20 (35.1) |
| Pericarditis | 14 (24.6) |
| Weight loss | 14 (24.6) |
| Lung disease | 1 (1.8) |
| Laboratory findings | |
| Leukocytosis (> 10,000/mm3) | 34 (59.7) |
| Neutrophils (> 80%) | 36 (63.2) |
| Hb < 90 g/L | 9 (15.8) |
| PLT < 100,000/mm3 | 2 (3.5) |
| ESR > 40 mm/h | 42 (73.7) |
| CRP > ULN | 54 (94.7) |
| Serum ferritin > 5 ULN | 36 (63.2) |
| Abnormal liver function | 36 (63.2) |
| Negative ANA (titer ≤ 1:80) | 54 (94.7) |
| Negative RF | 56 (98.2) |
| IL2R > ULN | 33/45 (73.3) |
| Pouchot score | 7 (5–7.5) |
Data are presented in the form of median (Q1–Q3) as continuous variable or as absolute number (percentage of the total patients%);
ULN upper limit of normal, Hb hemoglobin, PLT platelet, ESR erythrocyte sedimentation rate, ANA antinuclear antibody, RF rheumatoid factor, CRP C-reactive protein, IL-2R interleukin-2 receptor