Table 4.
Mortality in CDH affected live births for surveillance period 2001–2012.
| Country-Registry | Surveillance Period | Live Births with CDH | Age at Death | ||||||
|---|---|---|---|---|---|---|---|---|---|
| Day 1 | Day 2-Day 6 | Day 7-Day 27 | Day 28-Day 364 | Year 1–4 | Year 5 and Above | Kaplan-Meier Mortality Estimate (95% CI) | |||
| Hospital-Based Registries | |||||||||
| Argentina-RENAC1 | 2009–2012 | 133 | 48.9%4 | - | - | - | - | 48.9% (40.4, 57.4) | |
| Colombia-Bogotá2 | 2001–2012 | 70 | 20.0% | - | - | - | - | - | 20.0% (10.6, 29.4) |
| South America-ECLAMC1 | 2001–2012 | 663 | 0.2% | 50.1% | 5.6% | 0.9% | - | - | 56.7% (52.9, 60.5) |
| Spain-ECEMC | 2001–2012 | 94 | 7.4% | 4.3% | - | - | - | - | 11.7% (5.2, 18.2) |
| Mexico-RYVEMCE1 | 2001–2012 | 27 | 3.7% | 3.7% | - | - | - | - | 7.4% (0.0, 17.3)5 |
| Iran-TROCA | 2004–2012 | 90 | 2.2% | 0.0% | - | - | - | - | 2.2% (0.0, 5.3)5 |
| Israel-SMC3 | 2001–2012 | 39 | 23.1% | 7.7% | 17.9% | 5.1% | - | - | 53.8% (38.2, 69.5) |
| TOTAL | 1,116 | 3.0% | 36.3% | 3.9% | 0.7% | - | - | 45.1% (42.0, 48.1) | |
| Population-Based Registries | |||||||||
| Costa Rica-CREC1 | 2001–2012 | 135 | 6.7% | 37.0% | 6.7% | 2.2% | 2.2% | 0.0% | 54.8% (46.4, 63.2) |
| Czech Republic | 2001–2013 | 265 | 8.7% | 12.8% | 2.3% | 3.4% | 1.1% | 0.0% | 28.3% (22.9, 33.7) |
| France-Paris2 | 2001–2012 | 57 | 5.3% | 22.8% | 5.3% | - | - | - | 33.4% (21.1, 45.6) |
| Germany-Saxony Anhalt | 2001–2012 | 44 | 15.9% | 4.5% | 2.3% | 4.5% | 0.0% | 0.0% | 27.2% (14.1, 40.4) |
| Italy-Lombardy | 2003–2012 | 25 | 0.0% | 16.0% | 8.0% | - | - | - | 24.0% (7.2, 40.7) |
| Italy-Tuscany | 2001–2012 | 60 | 6.7% | 8.3% | 8.3% | 0.0% | - | - | 23.3% (12.6, 34.0) |
| Malta1 | 2001–2012 | 24 | 33.3% | 4.2% | 0.0% | 0.0% | 0.0% | 0.0% | 37.5% (18.1, 56.9) |
| Netherlands-Northern | 2001–2012 | 45 | 11.1% | 4.4% | 2.2% | 15.6% | 0.0% | 0.0% | 33.3% (19.5, 47.1) |
| Slovak Republic | 2001–2012 | 116 | 0.0% | 41.4% | 3.4% | - | - | - | 44.8% (35.8, 53.9) |
| Sweden | 2001–2012 | 278 | 10.4% | 3.6% | 2.9% | 5.4% | 1.1% | 0.4% | 23.8% (18.7, 28.7) |
| Ukraine-OMNI-Net | 2001–2012 | 62 | 16.1% | 21.0% | 0.0% | 6.5% | - | - | 43.6% (31.2, 55.9) |
| United Kingdom-Wales | 2001–2012 | 116 | 8.6% | 17.2% | 3.4% | 5.2% | 1.7% | 0.0% | 36.1% (27.5, 44.9) |
| USA-Arkansas | 2001–2012 | 139 | 14.4% | 10.8% | 4.3% | 2.9% | 2.2% | 0.0% | 34.6% (26.6, 42.4) |
| USA-Atlanta | 2001–2012 | 161 | 8.7% | 6.8% | 6.8% | 1.9% | 0.0% | 0.0% | 24.2% (17.6, 30.8) |
| USA-Texas | 2001–2012 | 1,240 | 8.3% | 9.4% | 8.5% | 7.7% | 1.4% | 0.1% | 35.4% (32.7, 38.0) |
| USA-Utah | 2001–2012 | 198 | 12.6% | 7.1% | 4.5% | 7.6% | 0.5% | 0.0% | 32.3% (25.8, 38.8) |
| TOTAL | 2,965 | 9.1% | 12.1% | 5.9% | 5.5% | 1.1% | 0.1% | 33.8% (32.1, 35.5) | |
| ALL REGISTRIES | 2001–2012 | 4,081 | 7.4% | 19.0% | 5.4% | 4.9% | 0.9% | 0.1% | 37.7% (36.2, 39.2) |
ETOPFA not allowed
ETOPFA not registered
data on live born children with congenital diaphragmatic hernia from one hospital
Percentage refers to first week mortality
Lower limit confidence intervals fitted to zero.
CI=Confidence Interval; CREC=Costa Rican Birth Defect Registry; ECEMC=Spanish Collaborative Study of Congenital Malformations; ECLAMC=Latin American Collaborative Study of Congenital Malformations; MCAR=Malta Congenital Anomalies Registry; OMNI-Net=Ukraine Birth Defects Prevention Program; RENAC=National Network of Congenital Anomalies of Argentina; RYVEMCE=Mexican Registry and Epidemiological Surveillance of External Congenital Malformations; TROCA=Tabriz Registry of Congenital Anomalies; SMC=Soroka Medical Center; USA=United States of America.