FIGURE 1.

NCS and skin biopsy evaluation. NCS of Patient 1 shows that the lateral femoral cutaneous nerve response is absent on the left (A) but normal on the right with a sensory nerve action potential amplitude of 11.8 μV (B). Skin biopsy of Patient 1 shows absent intraepidermal nerve fibers at the left proximal thigh (C) but rich epidermal innervation at the right proximal thigh (14.0 fibers/mm; normal ≥ 8) (D). E, Skin biopsy of Patient 2 shows absent IENF at the left proximal thigh. F, The IENF density is severely reduced with a few fibers present at the right proximal thigh (3.3 fibers/mm; normal ≥ 8) (arrows) [Color figure can be viewed at wileyonlinelibrary.com]