Table 3.

Most likely diagnoses in case 1.

5 most likely differential diagnoses (Q12)
1	Selected progressive p-cpacns	59/73	80.8%
2	Transient p-cpacns	51/73	69.9%
3	Ischaemic stoke	47/73	64.4%
4	Congenital anatomical deformity	29/73	39.7%
5	Infections	28/73	38.4%
6	Arteriovenous (AV) malformation	26/73	35.6%
7	CNS tuberculosis	24/73	32.9%
8	Migraine	11/73	15.1%
8	Tumo r	11/73	15.1%
10	Multiple sclerosis	4/73	5.5%
11	Traumatic intracranial bleeding	3/73	4.1%
Indicators of likely progressive p-cPACNS (Q13)
1	Imaging results, namely involvement of more than one vessel, involvement of distal segments, and posterior vessel affected	64/73	87.7%
2	Clinical course with disease progression over 3 months or more	51/73	69.9%
3	Laboratory findings suggesting systemic inflammation	34/73	46.6%
4	Acute presentation with “systemic signs”	32/73	43.8%
5	Response to immune modulation	30/73	41.1%