Table 2.
Characteristics of 58 AAV patients followed by the Rheumatology Clinic of Udine (2010–2018)
Demography | |
---|---|
Age, years | 57.8 ± 14.3 |
Female gender | 34 (58.6%) |
AAV diagnosis | |
GPA | 30 (51.7%) |
EGPA | 19 (32.8%) |
MPA | 9 (15.5%) |
BVAS v3 | 13.9 ± 6.7 |
Baseline vasculitis involvement | |
Constitutional symptoms | 47 (81%) |
ENT | 35 (60.3%) |
Lungs | 29 (50%) |
Kidney | 19 (32.8%) |
Nervous system | 19 (32.8%) |
Skin | 19 (32.8%) |
Cardiovascular | 6 (10.3%) |
Gastrointestinal | 6 (10.3%) |
Eye | 2 (3.4%) |
ANCA status | |
Positive ANCA | 47 (81%) |
cANCA/PR3 | 24 (51.1%) |
pANCA/MPO | 23 (48.9%) |
AAV ANCA-associated vasculitis, GPA granulomatosis with polyangiitis, EGPA eosinophilic granulomatosis with polyangiitis, MPA micropolyangiitis, BVAS Birmingham Vasculitis Activity Score, ENT ear-nose-throat involvement, ANCA anti-neutrophil cytoplasmic antibodies, PR3 proteinase 3, MPO myeloperoxidase. Variables are reported as mean ± SD or N (%)