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. 2020 Jul 14;16(3):581–589. doi: 10.1007/s11739-020-02431-y

Table 2.

Characteristics of 58 AAV patients followed by the Rheumatology Clinic of Udine (2010–2018)

Demography
Age, years 57.8 ± 14.3
Female gender 34 (58.6%)
AAV diagnosis
 GPA 30 (51.7%)
 EGPA 19 (32.8%)
 MPA 9 (15.5%)
 BVAS v3 13.9 ± 6.7
Baseline vasculitis involvement
 Constitutional symptoms 47 (81%)
 ENT 35 (60.3%)
 Lungs 29 (50%)
 Kidney 19 (32.8%)
 Nervous system 19 (32.8%)
 Skin 19 (32.8%)
 Cardiovascular 6 (10.3%)
 Gastrointestinal 6 (10.3%)
 Eye 2 (3.4%)
ANCA status
 Positive ANCA 47 (81%)
 cANCA/PR3 24 (51.1%)
 pANCA/MPO 23 (48.9%)

AAV ANCA-associated vasculitis, GPA granulomatosis with polyangiitis, EGPA eosinophilic granulomatosis with polyangiitis, MPA micropolyangiitis, BVAS Birmingham Vasculitis Activity Score, ENT ear-nose-throat involvement, ANCA anti-neutrophil cytoplasmic antibodies, PR3 proteinase 3, MPO myeloperoxidase. Variables are reported as mean ± SD or N (%)