Table 2.

Scoring system for detecting Marfan syndrome among BAV patients

Score	No	Yes
Mitral valve prolapse
Myopia ≥ 3DO
Pectus carinatum
Pes planus
Wrist and thumb signs
ΔAR-AA ≥ 4 mm
Total score*

The opportunity to refer the patient at a tertiary Center for MFS evaluation should be considered with a score ≥ 3

^*Each feature corresponds to a score of 1. Patients with a total score ≥ 3 have an Odds Ratio to be affected by MFS of 38.3 (95% CI 14.8–99.3)