Table 2.

Initial treatment.

Patient	Induction	Maintenance	Induction duration (days)a	Remission duration (days)b
1	IV high dose mPd 1 g	AZT, PD	42	751
2	PO PD 15 mg	PD	217	240
3	PO PD 20 mg	PD	599	3866
4c,d	PO PD 25 mg IV high dose CPM 300 mg every month (6 doses)	PD	222	215
5d	IV high dose mPd 700 mg over 3 days (3 doses) PO CPM 75 mg IVIG	PD	297	163
6d,e	IV high dose mPd 900 mg IV high dose CPM 740 mg every one month (4 doses)	PD, Cyclosporin	225	161
7d	IV high dose mPd 750 mg IV high dose CPM 750 mg every one month (6 doses) IVIG Infliximab 170 mg every 2 weeks (15 doses)	AZT, MTX, PD	206	117
8	PO PD 30 mg	AZT	49	189
9d	IV high dose mPd IV high dose CPM 500 mg every one month	AZT, PD	81	210

Initial treatment of nine patients. IV: intravenous; mPd: 6-methylprednisolone; AZT: azathioprine; PD: prednisolone; PO: oral administration; CPM: cyclophosphamide; IVIG: intravenous immunoglobulin G; MTX: methotrexate.

^aFrom the initial treatment to the start of steroid dose reduction.

^bFrom the start of maintenance therapy to the last follow-up or to the first relapse.

^cPatient 4 was treated with IVIG and several mPD pulse therapies before being diagnosed with PAN.

^dTreated with nifedipine ointment and alprostadil for Raynaud’s phenomenon.

^eOral cyclosporin A was used for maintenance and was stopped because of hypertensive encephalopathy.