FIGURE 1.
A, Pedigree of the present family. B, Sanger sequence chromatograms of the affected individuals (upper panel) or heterozygous carriers (lower panel) with PDCD6IP mutations. C, MRI of the proband, Sagittal T1-WI (I) shows microcephaly. Axial T1-WI and T2-WI (II, III) demonstrate a mildly simplified gyral pattern with normal cortical thickness. Axial T2-WI (IV) shows a disproportionally large cerebellum. D, Schematic representation of all 20 exons of the PDCD6IP gene. E, Known three structural and functional domains (Bro 1, V and Proline rich) of the mature PDCD6IP protein. Arrows show the position of the mutation (c.154_158dup; p.Val54Profs*18) identified in this study