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. 2021 Apr 17;22(8):4165. doi: 10.3390/ijms22084165
AD Alzheimer disease
ALS amyotrophic lateral sclerosis
APP amyloid beta precursor protein
BDNF brain-derived neurotrophic factor
CRM1 Chromosome region maintenance 1 protein
DPRs di-peptide repeat proteins
ER endoplasmic reticulum
FG repeats phenylalanine-glycine repeats
FISH fluorescence in situ hybridization
FUS fused in sarcoma
FTD frontotemporal dementia
hnRNPs heterogeneous nuclear ribonucleoproteins
HAP1 huntingtin associated protein 1
HD-RAN HD repeat-associated non-AUG translation
HTT Huntingtin
INM inner nuclear membrane
Kap Karyopherin
MAP2 microtubule-associated protein 2
MAPT microtubule-associated protein tau
mHTT mutant huntingtin
MNDs motor neuron diseases
mRNP messenger ribonucleoprotein
NCT nucleocytoplasmic transport
NDs neurodegenerative diseases
NE nuclear envelope
NEDD8 neural precursor cell-expressed and developmentally down-regulated 8
NES nuclear export sequence
NFTs neurofibrillary tangles
NLS nuclear localization sequence
NMJ neuromuscular junction
NPC nuclear pore complex
NTR nuclear transport receptors
Nups nucleoporins
O-GlcNAc O-linked N-acetylglucosamine
ONM outer nuclear membrane
PSEN1 presenilin1
PY-NLSs proline-tyrosine amino acid pairing
RAN Ras-related nuclear protein
RanBP1 Ran-binding protein 1
RanBP2/Nup358 Ran-binding protein 2/nucleoporin 358
RanBP3 Ran-binding protein 3
RanGAP Ran GTPase-activating protein
RanGEF Ran Guanine nucleotide Exchange Factor
RBPs RNA-binding proteins
RCC1 regulator of chromosome condensation 1
RNPs ribonucleoproteins
RNS Reactive nitrogen species
SFPQ splicing factor proline- and glutamine-rich
SOD1 superoxide dismutase-1
SORT1 sortilin
TARDBP transactive response DNA-binding protein
XPO1 Exportin-1