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. 2021 Apr 26;13(4):281–303. doi: 10.4252/wjsc.v13.i4.281

Table 2.

Main genes associated with inherited channelopathies

Condition
Genotype
Ref.
LQTS1 KCNQ1 [16]
LQTS2 KCNH2 [16]
LQTS3 SCN5A [16]
LQTS4 ANK2 [17]
LQTS5 KCNE1 [17]
LQTS6 KCNE2 [17]
LQTS7 KCNJ2 [17]
LQTS8 CACNA1C [17]
LQTS9 CAV3 [17]
LQTS10 SCN4B [17]
LQTS11 AKAP9 [17]
LQTS12 SNTA1 [17]
LQTS13 KCNJ5 [17]
LQTS14 CALM1 [17]
LQTS15 CALM2 [17]
JLN1 KCNQ1 [17]
JLN2 KCNE1 [17]
CPVT1 RYR2 [16]
CPVT2 CASQ2 [16]
SQTS KCNH2, KCNQ1, KCNJ2 [16]
BrS SCN5A [18]

BrS: Brugada syndrome; CPVT: Catecholaminergic polymorphic ventricular tachycardia; LQTS: Long QT syndrome; SQTS: Short QT syndrome.