Table 2.

Retrospective and original pathological diagnosis of Huntington’s disease (HD) in 195 cases with immunohistochemical analysis for HD inclusions.

HD inclusions†		Pathological diagnosis of HD
		Retrospective diagnosis				Original diagnosis
		+	–	HD‐like	NP	+	+?	–	NR
Positive	188	183‡	0	0	5	162	4	13	9
Negative	7	0	6	1§	0	1§	0	6	0

^† ubiquitinated N‐terminal huntingtin‐positive neuronal intranuclear and neuropil inclusions; + = positive; − = negative; +? = questionable; NP = not possible; NR = not reported.

^‡ Vonsattel et al’s grade (33, 49): 0 (1), I (4), II (36), III (93), IV (36), ungraded (13).

^§ Same case.