Table 1:
OI I | OI III | OI IV | OI V | Other/Unclassified | Total | |
---|---|---|---|---|---|---|
N | 173 | 49 | 80 | 5 | 13 | 320 |
Male n (%) | 45 (26) | 17 (35) | 33 (41) | 3 (60) | 7 (54) | 105 (33) |
Female (%) | 128 (74) | 32 (65) | 47 (59) | 2 40) | 6 (46) | 215 (67) |
Mean age in yrs at enrollment | 39.8 | 30.7 | 36 | 42.2 | 32.5 | 37.2 |
Median age (IQR) in yrs at enrollment | 37.8 (28.8–46.9) | 27.3 (21.3–32.5) | 33.4 (23.1–46.6) | 46.8 (31.3–50.4) | 29.1 (23.8–33.6) | 33.7 (25.3–46.6) |
Median L-spine aBMD Z-score (IQR) at enrollment* | −1.8 (−2.6 – −0.8) | −3.2 (−4.3 – −2.4) | −2.6 (−3.0 – −1.9) |
L-spine aBMD Z-scores available in 141, 22, and 48 individuals with OI types I, III, and IV, respectively.