Fig. 1.

Clinical characteristics (Axis I) (adapted from Albanese et al. 2013). In the upper part of the scheme, the four descriptors age at onset, body distribution, temporal pattern, and associated features are depicted with additional categories (temporal pattern) and all recommended subcategories. In the lower part, below the dark blue line, two sets of clinical descriptors are given as examples that are frequently seen in the clinic, although all other combinations of descriptions are possible, as well