Table 1.
Variable | n (%) or mean ± SD |
---|---|
Clinical and demographic data: | |
Saudi citizens | 11 (48) |
Female sex | 13 (57) |
Age at diagnosis (days) | 67 ± 37 |
Positive consanguinity | 12 (52) |
Family history of biliary atresia | 1 (4) |
Splenic malformation | 1 (4) |
Other malformations | 9 (39) |
Cardiovascular | 5 (21) |
Renal | 3 (13) |
Other (inguinal hernia) | 1 (4) |
Biochemical data: | |
Total bilirubin (µmol/L) | 165.8 ± 56.4 |
Direct bilirubin (µmol/L) | 131.6 ± 47.8 |
Alanine aminotransferase (U/L) | 166 ± 93 |
Aspartate aminotransferase (U/L) | 240 ± 139 |
Alkaline phosphatase (U/L) | 815 ± 405 |
Albumin (g/L) | 33 ± 5 |
Gamma glutamyl transferase (U/L) | 530 ± 318 |
Impaired synthetic function | 3 (14) |
25-OH Vitamin D (nmol/L) | 19 ± 16.8 |
SD, standard deviation.