| aa | amino acid |
| ALS | amyotrophic lateral sclerosis |
| AMP | adenosine 3′, 5′-monophosphate |
| AMPA | α-amino-3-hydroxy-5-methyl-4-isoxazolepropinionic acid |
| AMPK | AMP-activated protein kinase |
| Ca2+ | calcium |
| CK1 | casein kinase 1ε |
| CTF | C-terminal fragment |
| eIF2α | eukaryotic initiation factor 2 alpha |
| EEAT2 | excitatory amino acid transporter 2 |
| ENU | N -ethyl-N-nitrosurea |
| ER | endoplasmic reticulum |
| FTD-TDP | frontotemporal degeneration associated with TDP-43 pathology |
| FTLD | frontotemporal lobar degeneration |
| G3BP | RasGAP-association endoribonuclease |
| G4-RNA | G-quadruplex-RNA |
| GSK-3β | glycogen synthase kinase 3β |
| LLPS | liquid–liquid phase separation |
| MALAT | metastasis-associated lung adenocarcinoma transcript 1 (also known as NEAT2; nuclear paraspeckle assembly transcript 2) |
| miRNA | micro RNA |
| mRNA | messenger ribonucleic acid |
| mTOR | mammalian target of rapamycin |
| NEAT1 | nuclear paraspeckle assembly transcript 1 |
| NES | nuclear export signal |
| NeuN | neuronal nuclei |
| neuroLNC | neuron-specific long-non-coding RNA |
| NLS | nuclear localization signal |
| NMJ | neuromuscular junction |
| PARP-1 | poly-(ADP-ribose) polymerase-1 |
| PINK1 | PTEN-induced putative kinase 1 |
| PP2A | protein phosphatase 2A |
| PSF | proline-glutamine rich |
| PTM | post-translational modification |
| RBP | RNA-binding protein |
| RNA | ribonucleic acid |
| RNS | reactive nitrogen species |
| ROS | reactive oxygen species |
| RRM | RNA recognition motif |
| SURF | SMG1, UPF1 and eRF1 and 2 |
| TARDBP | TAR-DNA-binding protein 43 |
| TBK1 | tank-binding kinase 1 |
| TDP-43 | TAR-DNA-binding protein 43 |
| TFEB | transcription factor EB |
| TIA-1 | T-cell intracellular antigen 1 |
| UPR | unfolded protein response |
| UPS | ubiquitin proteasome system |