Table 1:

Characteristics of the cohort at enrollment and follow-up (N=1734).

Characteristic		% (N) or Median (IQR)
Gender	Female	49% (854)
Race	Caucasian	95% (1648)
Ethnicity 1	Non-Hispanic	91.9% (1593)
	Unknown	4% (70)
CFTR mutations	Two alleles F508del	51% (890)
	One allele F508del	39% (669)
	Other or unknown	10% (175)
Weight percentile		36.7 (16.5-63.4)
Follow-up, years		7.8 (6.3-8.3)
Occurrence of one or more PExs during follow-up		45% (788)
Number of PExs recorded during follow-up		0 (0-2)
PEx annual rate during follow-up		0 (0-0.3)
Age at enrollment, years		5.8 (3-8.8)
Age at end of follow-up, years		12.7 (9.7-16)

¹Hispanic is the reference.