Table 1.
Demographic and clinical features of patients with PFAPA syndrome.
| Demographic features n (%) | |
|---|---|
| Age at onset (median years; IQR) | 4; 1–7 |
| Age at colchicine initiation (median years; IQR) | 6; 3–9.5 |
| Sex (M/F) | 6/7 |
| Clinical features | |
| Aphthous stomatitis | 8 (61) |
| Pharyngitis | 11 (84) |
| Cervical adenitis | 9 (69) |
| Abdominal pain | 5 (38) |
| Diarrhea | 0 (0) |
| Thoracic pain | 0 (0) |
| Headaches | 0 (0) |
| Arthritis/skin rash | 0 (0) |
| Arthralgia | 2 (15) |
| Myalgia | 0 (0) |
| Symptomatic intervals between episodes | 0 (0) |
| Neutropenia | 0 (0) |
| Increased inflammatory markers during attacks | 13 (100) |
| Normal inflammatory markers during fever-free Intervals | 13 (100) |
IQR: interquartile range; M: male; F: female.