Table 1.
Case No. | Age (years) |
Sex | Signs and symptoms | Imaging findings | Histomorphological features | Treatment & follow up |
---|---|---|---|---|---|---|
1 | 40 | F | Right sided nasal mass | Nasal mass with intracranial extension | Papillary pattern, perivascular arrangement, basaloid morphology, necrosis | NA |
2 | 38 | M | Swelling below left orbit | Mass in the maxillary sinus with extension into inferior orbital wall and infra-temporal fossa | Sheets of large cells with moderate cytoplasm, vesicular nucleus & conspicuous nucleoli | NA |
3 | 17 | M | Nasal mass with left cervical LN | CECT face and neck-large heterogeneously enhancing infiltrative soft tissue lesion centred in left nasopharynx, pterygo-maxillary space, left hemisphenoid, parasellar, paraclival region & left maxillary antrum | Diffuse infiltrative pattern, Trabecular and cords of tumor cells, small cell carcinoma like pattern |
No surgery, treated with chemo & radiotherapy DOD, 3 months after the biopsy diagnosis |
4 | 27 | M | Right sided nasal mass of 2-year duration | CECT–small polypoidal enhancing lesion extending from anterior aspect of inferior turbinate with contiguous extension to lateral nasal wall | Diffuse and nest like patterns, sarcomatoid areas, focal rhabdoid morphology | WLE of the mass. Alive without any recurrence (2 years duration) |
5 | 33 | M | Right sided polypoidal nasal mass | NA | Single cells, small nest, sheets of tumor cells variable amount of cytoplasm, round vesicular nucleus and prominent nucleoli, lymphoma like morphology | NA |
6 | 50 | M | Left nasal obstruction, bleeds on touch | NA | Nest of large tumor cells with moderate amount of cytoplasm, round nuclei & conspicuous nucleoli | Treatment details were not available. DOD, 1 year after the diagnosis |
SNUC sinonasal undifferentiated carcinoma, SDSC SMARCB1/INI1 deficient sinonasal carcinoma, NA not available, DOD died of diseases, WLE wide local excision