Table 1.
Clinical features of the 35 patients with PSC at the time of diagnosis.
| Feature | Value∗ |
|---|---|
| Male sex | 14 (40.0) |
| Age† | 27 (22–38) |
| Type of PSC | |
| Large-duct PSC | 28 (80.0) |
| Small-duct PSC | 3 (8.6) |
| PSC-AIH variant | 4 (11.4) |
| Localisation of bile duct changes in large-duct PSC | |
| Intrahepatic only | 8 (26.7) |
| Intrahepatic and extrahepatic | 16 (53.3) |
| Extrahepatic only | 6 (20.0) |
| Cirrhosis at diagnosis | 2 (5.7) |
| Inflammatory bowel disease | |
| Ulcerative colitis | 13 (37.1) |
| Crohn disease | 5 (14.3) |
| Absence of IBD | 17 (48.6) |
AIH, autoimmune hepatitis; IBD, inflammatory bowel disease; PSC, primary sclerosing cholangitis.
∗
Categorical variables are described as frequency (%).
†
Age is reported as median (IQR).