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. 2021 May 25;14:84. doi: 10.1186/s13041-021-00795-6

Table 1.

Proteins involved in mitochondrial pathways affected in Ts1Cje SNs

Symbol Entrez gene name ID Ts1Cje Pathway
APP Amyloid beta precursor protein P12023 1.246

Mitochondrial dysfunction

Sirtuin signaling

ATP5MF ATP synthase membrane subunit f P56135 1.925

Mitochondrial dysfunction

Oxidative phosphorylation

ATP5PD ATP synthase peripheral stalk subunit d Q9DCX2 1.523

Mitochondrial dysfunction

Oxidative phosphorylation

ATP5PF ATP synthase peripheral stalk subunit F6 P97450 1.907

Mitochondrial dysfunction

Oxidative phosphorylation

Sirtuin signaling

COX4I1 Cytochrome c oxidase subunit 4I1 P19783 1.818

Mitochondrial dysfunction

Oxidative phosphorylation

COX5A Cytochrome c oxidase subunit 5A P12787 1.889

Mitochondrial dysfunction

Oxidative phosphorylation

Cox6c Cytochrome c oxidase subunit 6C Q9CPQ1 2.119

Mitochondrial dysfunction

Oxidative phosphorylation

CYC1 Cytochrome c1 Q9D0M3 1.728

Mitochondrial dysfunction

Oxidative phosphorylation

Sirtuin signaling

CYCS Cytochrome c. somatic P62897 1.976

Mitochondrial dysfunction

Oxidative phosphorylation

GPD2 Glycerol-3-phosphate dehydrogenase 2 Q64521 1.549 Mitochondrial dysfunction
MAOB Monoamine oxidase B Q8BW75 1.235 Mitochondrial dysfunction
MT-CO2 Cytochrome c oxidase subunit II P00405 2.804

Mitochondrial dysfunction

Oxidative phosphorylation

NDUFA2 NADH:ubiquinone oxidoreductase subunit A2 Q9CQ75 1.337

Mitochondrial dysfunction

Oxidative phosphorylation

Sirtuin signaling

NDUFA4 NDUFA4 mitochondrial complex associated Q62425 1.331

Mitochondrial dysfunction

Oxidative phosphorylation

Sirtuin signaling

NDUFA8 NADH:ubiquinone oxidoreductase subunit A8 Q9DCJ5 1.546

Mitochondrial dysfunction

Oxidative phosphorylation

Sirtuin signaling

NDUFAF1 NADH:ubiquinone oxidoreductase complex assembly factor 1 A2AQ17 1.359

Mitochondrial dysfunction

Sirtuin signaling

NDUFS1 NADH:ubiquinone oxidoreductase core subunit S1 Q91VD9 1.813

Mitochondrial dysfunction

Oxidative phosphorylation

Sirtuin signaling

NDUFS3 NADH:ubiquinone oxidoreductase core subunit S3 Q9DCT2 1.713

Mitochondrial dysfunction

Oxidative phosphorylation

Sirtuin signaling

NDUFS6 NADH:ubiquinone oxidoreductase subunit S6 P52503 1.368

Mitochondrial dysfunction

Oxidative phosphorylation

Sirtuin signaling

NDUFV2 NADH:ubiquinone oxidoreductase core subunit V2 Q9D6J6 1.487

Mitochondrial dysfunction

Oxidative phosphorylation

Sirtuin signaling

SLC25A4 Solute carrier family 25 member 4 P48962 1.591 Sirtuin signaling
UQCRB Ubiquinol-cytochrome c reductase binding protein Q9CQB4 1.928

Mitochondrial dysfunction

Oxidative phosphorylation

UQCRC1 Ubiquinol-cytochrome c reductase core protein 1 Q9CZ13 1.687

Mitochondrial dysfunction

Oxidative phosphorylation

UQCRFS1 Ubiquinol-cytochrome c reductase. Rieske iron-sulfur polypeptide 1 Q9CR68 3.192

Mitochondrial dysfunction

Oxidative phosphorylation

Sirtuin signaling

UQCRQ Ubiquinol-cytochrome c reductase complex III subunit VII Q9CQ69 2.522

Mitochondrial dysfunction

Oxidative phosphorylation

VDAC1 Voltage dependent anion channel 1 Q60932 1.762

Mitochondrial dysfunction

Sirtuin signaling

VDAC2 Voltage dependent anion channel 2 Q60930 2.043

Mitochondrial dysfunction

Sirtuin signaling

WRN Werner syndrome RecQ like helicase O09053 − 1.341 Sirtuin signaling

The relative amounts (fold change, compared to WT SNs) of these proteins in Ts1Cje SNs are shown