Table 3.
Respiratory parameters recorded using PSG.
| Patients with OSAS n = 87 (80.5%) |
Respiratory Characteristics in Polysomnography Median [IQR] |
||||
|---|---|---|---|---|---|
| AHI (events/h) | Index > 3% (ODI/h) | SpO2 < 90% n (%) * | SatO2 Nadir (%) | ||
| Neuromuscular disorders |
59
(67.8%) |
41
(69.4%) |
|||
| Spinal muscular atrophy (SMA) | 29 | 8.3 [3.1–15.9] | 4.8 [2.9–1.7] | 22 | 77 |
| Duchenne muscular dystrophy | 23 | 6.3 [6.3–9.5] | 6.2 [2.9–0.5] | 13 | 80 |
| Ulrich muscular dystrophy | 1 | 16 | 16.4 | 1 | 85 |
| Merosin deficient muscular dystrophy | 1 | 8.3 | 6.9 | 1 | 89 |
| Other myopathies | 5 | 13 [5.8–16.3] | 15.3 [7.2–2.1] | 4 | 82 |
| Skeletal disorders |
4
(4.6%) |
4
(100%) |
|||
| Achondroplasia (ACH) | 3 | 6.5 [3–117.5] | 9.3 [5.3–100.3] | 3 | 71 |
| Marfan syndrome | 1 | 8.4 | 6.1 | 1 | 84 |
| Complex abnormalities |
24
(27.5%) |
17
(70.8%) |
|||
| Craniosynostosis (Crouzon syndrome) | 2 | 27.5 [17.3–37.8] | 26.7 [26.2–27.2] | 2 | 60 |
| Prader–Willi syndrome (PWS) | 18 | 5.7 [3.7–9.6] | 7.6 [5,6,7,8,9,10,11,12,13,14,15] | 14 | 73 |
| Arnold–Chiari syndrome | 4 | 5.1 [1.3–9.1] | 16.5 [15.1–17.5] | 1 | 70 |
IQR: interquartile range. Obstructive apnea–hypopnea index (AHI) events/h. Oxygen desaturation index > 3% (ODI)/h. Number of patients with SpO2 < 90% is given as n (%), * percent from the group of disorders.