Table 2.
2008 IWG-MRT diagnostic criteria for post-PV/ET MF [16].
| Required criteria Additional criteria | (1) Documentation of a previous diagnosis of ET or PV as defined by WHO criteria (2) Bone marrow fibrosis grade 2/3 (on a 0–3 scale or grade 3/4 (on a 0–4 scale) |
| Additional criteria Post-PV MF | (1) Anemia or sustained loss of requirement for either phlebotomy or for cytoreductive treatment (2) Leukoerthryoblastic peripheral blood smear (3) Increasing splenomegaly of ≥5 cm (distance of the tip of the spleen from the left costal margin) or appearance of new splenomegaly (4) Development of ≥1 of 3 constitutional symptoms: >10% weight loss, night sweats, or unexplained fever >37.5 °C |
| Post-ET MF | (1) Anemia and a 2 mg/ml decrease from baseline hemoglobin level (2) Leukoerythroblastic peripheral blood smear (3) Increasing splenomegaly of ≥5 cm (distance of the tip of the spleen from the left costal margin) or appearance of new splenomegaly (4) Increased lactate dehydrogenase (above reference level) (5) Development of ≥1 of 3 constitutional symptoms: >10% weight loss, night sweats, or unexplained fever >37.5 °C |
Diagnosis requires presence of required criteria and 2 additional criteria.