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. 2021 May 27;11:11135. doi: 10.1038/s41598-021-90590-z

Table 1.

Candidate variants in the discovery cohort.

Gene Variant description Patient Relevance
CHAD NM_001267:c.1049C > T:p.(T350I) PC-005;PC-015 PI3K-Akt pathway; present in individual with diagnosis before 40y; gene described in early-onset literature16
CHD1L NM_004284:c.2398delT:p.(L800X) PC-012 Loss-of-function variant; gene described in early-onset literature17
ERCC6 NM_000124:c.3437_3438insAAG:p.(S1146delinsRS) PC-013 Nucleotide Excision Repair (NER); loss-of-function variant; gene described in early-onset literature18
ITGB7 NM_000889:c.1063_1066del:p.(V355fs) PC-008 PI3K-Akt pathway; loss-of-function variant; gene described in early-onset literature16,19
PTPN13 NM_080685:c.4258 + 2 T > C PC-008 Apoptosis; other gene family members have been described as potential candidates for CRC susceptibility16
SPATA20 NM_022827:c.151C > T:p.(R51X) PC-015 Present in individual with diagnosis before 40y; loss-of-function variant; gene described in early-onset literature16,19
TDG NM_003211:c.67C > T:p.(Q23X) PC-018 Base Excision Repair (BER); loss-of-function variant; gene described in early-onset literature17
TGS1 NM_024831:c.439_444del:p.(147_148del) PC-017 Peroxisome Proliferator-activated Receptors (PPAR) pathway; gene described in early-onset literature17

Potential risk genes identified in the discovery cohort and selected for replication, with their corresponding detected rare, high-impact changes.