Table XI.

Tumors of uncertain differentiation.

Benign

Myxoma (cellular myxoma)

Deep (aggressive) angiomyxoma

Pleomorphic hyalinising angiectatic tumour

Phosphaturic mesenchymal tumour

Perivascular epithelioid tumour, benign

Angiomyolipoma

Intermediate (locally aggressive)

Haemosiderotic fibrolipomatous tumour

Angiomyolipoma, epithelioid

Intermediate (rarely metastasising)

Atypical fibroxanthoma

Angiomatoid fibrous histiocytoma

Ossifying fibromyxoid tumour

Myoepithelioma

Malignant

Phosphaturic mesenchymal tumour, malignant

NTRK-rearranged spindle cell neoplasm (emerging)

Synovial sarcoma

Epithelioid sarcoma: proximal and classic variant

Alveolar soft part sarcoma

Clear cell sarcoma

Extraskeletal myxoid chondrosarcoma

Desmoplastic small round cell tumour

Rhabdoid tumour

Perivascular epithelioid tumour, malignant

Intimal sarcoma

Ossifying fibromyxoid tumour, malignant

Myoepithelial carcinoma

Undifferentiated sarcoma

Spindle cell sarcoma, undifferentiated

Pleomorphic sarcoma, undifferentiated

Round cell sarcoma, undifferentiated