Table 3.

Contents of Gb3 and Lyso-Gb3 in organs and tissues of wild-type and Fabry mice.

	Wild-type [n = 4]		Fabry [n = 4]
	Gb3 (μg/g)	Lyso-Gb3 (nmol/g)	Gb3 (μg/g)	Lyso-Gb3 (nmol/g)
Liver
Not treated	1.0 ± 0.0	0.08 ± 0.01	155 ± 15	7.3 ± 0.6
Hydroxychloroquine	1.0 ± 0.0	0.06 ± 0.01	145 ± 12	6.7 ± 0.3
Amiodarone	1.0 ± 0.0	0.06 ± 0.01	169 ± 9	7.6 ± 0.9
Kidneys
Not treated	15 ± 3	0.08 ± 0.01	165 ± 12	2.0 ± 0.3
Hydroxychloroquine	13 ± 2	0.08 ± 0.01	156 ± 10	1.9 ± 0.1
Amiodarone	14 ± 1	0.09 ± 0.02	160 ± 16	2.1 ± 0.2
Heart
Not treated	0.5 ± 0.0	0.09 ± 0.02	37 ± 6	0.59 ± 0.11
Hydroxychloroquine	0.5 ± 0.0	0.10 ± 0.01	38 ± 3	0.58 ± 0.55
Amiodarone	0.5 ± 0.0	0.08 ± 0.01	40 ± 3	0.59 ± 0.07

Data are expressed as means ± SD.