Timely cochlea implantations in family SB162 rescue impaired speech discrimination. (A) Longitudinal change of postoperative auditory performance from control subjects (n = 39) with adult-onset progressive hearing loss. (B) Speech discrimination performance scores of subject #284 measured at 3, 6, and 12 mo following cochlear implantation. (C) Speech discrimination performance scores of subject #291 measured at 1.5 mo following cochlear implantation. K-CID Sentence score, Korean Central Institute for the Deaf score; PB word score, Phonetically Balanced word score; Spondee words, a word with two syllables—disyllabic, that is, pronounced with equal emphasis on first and second syllables.