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. 2021 Jun 10;11:12278. doi: 10.1038/s41598-021-91671-9

Table 3.

Diagnostic methods according to Whipple disease entity.

CWD
N = 11
LWD
N = 24
AWD
N = 15
PAWD
N = 18
Total
N = 68
PAS staining n/N (%) 11/11 (100) 0/12 (0) 0/15 (0) ND
PCR n/N (%)
Cutaneous biopsy 2/2 (100) 0/2 (0) 0/1 (0) 3/8 (38) 5/13 (38)
Saliva 10/11 (91) 15/21 (71) 13/16 (81) 14/18 (78) 52/66 (79)
Stool 9/9 (100) 21/22 (95) 14/14 (100) 17/18 (94) 61/63 (97)
Saliva and stool 9/9 (100) 15/21 (71) 12/14 (86) 13/18 (72) 49/62 (79)
Small-bowel biopsy 8/9 (89) 7/17 (41) 8/14 (57) 10/11 (91) 33/51 (65)
Synovial fluid 3/5 (60) 21/21 (100) 0/1 (0) 0/1 (0) 24/28 (86)
Synovial biopsy 1/1 (100) 1/2 (50) 0/1 (0) 0/1 (0) 2/5 (40)
Discovertebral biopsy 0 1/2 (50) 0/1 (0) 0 1/3 (33)
CSF 1/6 (17) 3/11 (27) 0/5 (0) 0/9 (0) 4/31 (13)
Cardiac valve 1/1 (100) 0 0 0 1/1 (100)
Urine 1/3 (33) 0/3 (0) 1/2 (50) 0/3 (0) 2/11 (18)
Blood 5/10 (50) 2/9 (22) 2/4 (50) 1/9 (11) 10/32 (31)

AWD arthropathic Whipple disease; CSF cerebrospinal fluid; CWD classic Whipple disease; LWD localized Whipple disease; PAS periodic acid-Schiff; PAWD probably athropathic Whipple disease.