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. 2021 Jun 11;22:438. doi: 10.1186/s12864-021-07758-0

Fig. 3.

Fig. 3

A. Normal appearing myofibrils adjacent to myofibrils with Z-disc disruption (arrow) and myofilament disarray in an MFM WB. 10 k. B. Marked myofilament disarray and ectopic accumulation of Z-disc material in an MFM WB. 10 k. C. Higher magnification of B. highlighting Z disc protein aggregation (arrow). 40 k. D. Mitochondria showing variability in size and cristae formation in an MFM WB. 27 k