| AChR | acetylcholine receptor |
| AIM2 | absent in melanoma 2 |
| AKT | Protein kinase B |
| ALS | Amyotrophic lateral sclerosis |
| Ang II | angiotensin II |
| AP-1 | activator protein-1 |
| ASC | apoptosis-associated speck-like protein containing a CARD |
| ATP | Adenosine triphosphate |
| BBB | blood-brain barrier |
| Ca2+ | calcium ions |
| CARD | caspase recruitment domain |
| CAPS | cryopyrin-associated periodic syndromes |
| cGAS | cytoplasmic DNA sensor cyclic guanosine monophosphate (GMP)-AMP synthase |
| CK | creatine kinase |
| CMT | Charcot-Marie-tooth |
| CNS | central nervous system |
| COP | Card-only protein |
| COX | cyclo-oxygenase |
| CRISPR | clustered regularly interspaced short palindromic repeats |
| DAMP | damage-associated molecular pattern |
| DAPC | dystrophin-associated protein complex |
| DM | dermatomyositis |
| DMD | Duchenne Muscular Dystrophy |
| EAMG | experimental autoimmune MG |
| EDL | extensor digitorum longus |
| FUS | fused in sarcoma |
| GFAP | glial fibrillary acidic protein |
| GLT-1 | glutamate transporter-1 |
| GRMD | golden retriever model of DMD |
| GSDMD | gasdermin-D |
| GT1 | glutamate transporter 1 |
| GTP | guanosine triphosphate |
| ICAM-1 | intercellular adhesion molecule-1 |
| IFNγ | Interferon gamma |
| IL | Interleukin |
| iPSC | induced pluripotent stem cell |
| JAK2 | janus kinase 2 |
| K+ | potassium ions |
| KO | Knockout |
| LGMD | Limb–girdle muscular dystrophy |
| LGMD2B | Limb-girdle muscular dystrophy type 2B |
| LPS | Lipopolysaccharides |
| LRR | leucine rich repeats |
| MAO-B | monoamine oxidase B |
| Mdx | X-linked muscular dystrophy |
| Mt | Mitochondrial |
| mTOR | mechanistic target of rapamycin |
| Myd88 | myeloid differentiation primary response gene 88 |
| NAIP | Neuronal apoptosis inhibitory protein |
| NEK7 | NIMA-related kinase 7 |
| NF-κB | nuclear factor kappa B |
| NLRC4 | NOD-like receptor family CARD domain-containing protein 4 |
| NLRP | NOD-like receptors with pyrin domain |
| NM | necrotizing myopathy |
| NO | nitric oxide |
| NOD | nucleotide-binding oligomerization domain |
| NOD2 | nucleotide-binding oligomerization domain-containing protein 2 |
| NAMP | neurodegeneration-associated molecular pattern |
| NSAID | nonsteroidal anti-inflammatory drug |
| OM | overlap myositis |
| P2X7 | purinergic type 2 receptor family |
| PAMP | pathogen-associated molecular pattern |
| PI3K | Phosphoinositide 3-kinase |
| PM | polymyositis |
| POP | Pyrin-only protein |
| Pro-IL | pro-interleukin |
| PYD | pyrin domain |
| RIP2 | receptor-interacting-serine/threonine-protein kinase 2 |
| ROS | reactive oxygen species |
| SASP | senescence-associated secretory phenotype |
| SOD1 | superoxide dismutase 1 |
| STAT3 | signal transducer and activator of transcription 3 |
| TA | tibialis anterior |
| TDP-43 | TAR DNA-binding protein 43 kDa |
| TLR | toll-like receptor |
| TNF-α | tumor necrosis factor-α |
| Tregs | regulatory T-lymphocyte |
| VBP15 | Vamorolone |
| VCAM-1 | vascular cell adhesion molecule |
| WT | wild-type |