Table 2. Clinical investigations.
| Findings on ECG | Median (IQR) | n (%) |
| P | 0 | |
| Right-axis deviation | 1 (5) | |
| S wave in standard lead 1 | 3 (15) | |
| Q wave in standard lead 3 | 2 (10) | |
| T wave in standard lead 3 | 1 (5) | |
| R wave in ventricular lead 1 | 1 (5) | |
| RVH | 0 | |
| RV strain | 1 (5) | |
| RBBB | 0 | |
| Findings on chest X-ray | ||
| Elevated cardiac apex | 10 (50) | |
| Enlarged right atrium | 10 (50) | |
| Enlarged pulmonary arteries | 15 (75) | |
| Pruning of peripheral pulmonary vessels | 5 (25) | |
| Pleuro-parenchymal bands | 12 (60) | |
| Volume loss | 2 (10) | |
| Tracheal deviation | 0 | |
| Spirometry | ||
| FEV1 | 2.77 (2.29 - 3.31) | |
| FVC | 3.41 (2.82 - 3.96) | |
| Ratio | 82.85 (73.10 - 86.85) | |
| DLCO (%Pred) | 99.5 (84.5 - 108.5) | |
| Low DLCO | 3 (15) | |
| Room air saturation | 96 (95.5 - 97.0) | |
| Echocardiography | ||
| LVIDd (mm) | 43.5 (41.5 - 48.5) | |
| LVIDs (mm) | 28 (27.5 - 30) | |
| LVEF (%) | 60 (56 - 64) | |
| RWMA | 0 | |
| Left atrium (mm) | 27.5 (23 - 31) | |
| Ascending aorta (mm) | 23 (21 - 26.5) | |
| E/a | 1.24 (1 - 1.50) | |
| E/e | 6 (5.19 - 8.30) | |
| Diastolic dysfunction | 3 (15) | |
| Aortic regurgitation | 1 (5) | |
| Aortic stenosis | 0 | |
| Mitral regurgitation | 2 (10) | |
| Mitral stenosis | 0 | |
| Tricuspid regurgitation | 5 (25) | |
| TAPSE (mm) | 21 (19 - 23) | |
| TAPSE <16 mm | 0 | |
| PASP (mmHg) | 18 (8.5 - 24.5) | |
| RAP (mmHg) | 5 (3 - 9.5) | |
| IVC (mm) | 14 (13 - 18) | |
| NT-proBNP | 26 (16 - 66) |
ECG = electrocardiography
IQR = interquartile range
P = pulmonale
R = right-axis deviation
RVH = right ventricular hypertrophy
RV = right ventricular
RBBB = right bundle branch block
FEV1 = forced expiratory volume in one second
FVC = forced vital capacity
DLCO = diffusing capacity of lung for carbon monoxide
LVIDd = left ventricular internal diameter end diastole
LVIDs = left ventricular internal diameter end systole
LVEF = left ventricular ejection fraction
RWMA = regional wall motion abnormality
TAPSE = tricuspid annular plane systolic excursion
PASP = pulmonary hypertension echocardiography
RAP = right arterial pressure
IVC = inferior vena cava
NT-proBNP = N-terminal pro-B-type natriuretic peptide