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. 2021 Jun 1;12:678953. doi: 10.3389/fimmu.2021.678953

Table 3.

Biological functions of histone citrullination.

Histone PAD isozyme Physiological or pathological roles References
Linker H1Cit54 PAD4 impairs binding to nucleosomal DNA (130, 131)
chromatin decondensation in pluripotent stem cells
H2ACit3 PAD4 occurs in calcium ionophore A23187-stimulated neutrophils (77, 132)
H3Cit2,8,17 PAD1 facilitates early embryo genome transactivation (133)
H3Cit2,8,17 PAD2 regulates lactation associated genes during diestrus in mammary epithelial cells (69)
H3Cit2,8,17 PAD4 neutrophil extracellular trap (NET) formation and NETosis (134, 135)
H3Cit8 PAD4 transcriptional repression of cytokines genes and human endogenous retroviruses (HERVs) via heterochromatin protein 1α (HP1α) (136)
H3Cit26 PAD2 chromatin decondensation and transcriptional activation of estrogen receptor (ER) α-regulated gene (68)
potential prognostic biomarker for ER positive (ER+) breast cancer (137)
H4Cit3 PAD4 facilitates early embryo genome transactivation (133)
regulates p53 pathway in apoptosis and in carcinogenesis (81)
neutrophil extracellular trap (NET) formation and NETosis (1214, 134)

H, histone; Cit, citrullination; PAD, peptidylarginine deiminase.