Table 3.
Interictal epileptic discharges (IEDs) in CACNA1A patients
Pt. ID | Phenotype | Age at onset | Age at EEG | IEDs |
---|---|---|---|---|
1-IV | FHM1 | 1 | 11 | Bilateral frontal sharp waves |
2-I | EA2 | 1 | Childhood* | Generalized spike waves |
4-III | EA2 | 2 | 15 | Generalized spike wave complexes |
4-IV | EA2 | 10 | 20 | Superimposed spikes in generalized rhythmic delta |
4-V | EA2 | 1 | 26 | Left temporal sharp waves |
4-VI | EA2 | 1 | 3 | Superimposed spikes in generalized rhythmic delta |
5-I | EA2 | 1 | 30 | Left temporal sharp waves |
15-I | EA2 | 1 | 6 | Superimposed spikes in generalized rhythmic delta |
*The first rsEEG at our department was performed at 28 years of age. IEDs were documented in previous EEGs