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. 2021 Jun 9;12:666273. doi: 10.3389/fimmu.2021.666273

Table 4.

Clinical manifestations of the patients.

Clinical manifestations in 46 patients
n (%) n (%)
Constitutional Symptoms Cardiorespiratory
Fever (>38C) 38 (82.6%) Thoracic pain 9 (19.6%)
Headache 10 (21.7%) Pleurisy 3 (6.5%)
Fatigue 15 (32.6%) Pericarditis 1 (2.2%)
Musculoskeletal Lymphoid
Skeletal dysplasia 1 (2.2%) Lymphadenopathy 8 (17.4%)
Skull anomaly 1 (2.2%) Splenomegaly 7 (15.2%)
Overgrowth patella 1 (2.2%) Gastrointestinal
Myalgias 18 (39.1%) Abdominal pain 24 (52.2%)
Arthralgia 24 (52.2%) Peritoneal adhesion 2 (4.3%)
Arthritis 7 (15.2%) Constipation 4 (8.7%)
Mucocutaneous Diarrhea 11 (23.9%)
Aphthous stomatitis 6 (13%) Vomiting 9 (19.6%)
Exudative pharyngitis 5 (10.9%) Ocular
Cold urticaria 1 (2.2%) Conjunctivitis 4 (8.7%)
Maculo-papular rash 11 (23.9%) Keratitis 2 (4.3%)
Urticarial rash 6 (13%) Periorbital edema 5 (10.9%)
Erysipelas-like rash 2 (4.3%) Visual loss 1 (2.2%)
Pseudo-folliculitis 2 (4.3%)