Figure 1.
Diagnosis algorithm of Castleman disease. Abbreviation: ALPS, autoimmune lymphoproliferative syndrome; AOSD, adult-onset Still’s disease; EBV, Epstein-Barr virus; FDC sarcoma, follicular dendritic cell sarcoma; HHV-8, human herpesvirus 8; HIV, human immunodeficiency virus; IPL, idiopathic plasmacytic lymphadenopathy; KSHV, Kaposi’s sarcoma-associated herpesvirus; RA, rheumatoid arthritis; SLE, systemic lupus erythematosus.