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. 2021 Jun 11;22(12):6286. doi: 10.3390/ijms22126286

Figure 1.

Figure 1

Diagnosis algorithm of Castleman disease. Abbreviation: ALPS, autoimmune lymphoproliferative syndrome; AOSD, adult-onset Still’s disease; EBV, Epstein-Barr virus; FDC sarcoma, follicular dendritic cell sarcoma; HHV-8, human herpesvirus 8; HIV, human immunodeficiency virus; IPL, idiopathic plasmacytic lymphadenopathy; KSHV, Kaposi’s sarcoma-associated herpesvirus; RA, rheumatoid arthritis; SLE, systemic lupus erythematosus.