Table 1.
Clinical characteristics of patients with T cell-EBV-HLH
Patient number | Gender | Ethnic background* | Family history | Age at presentation (years) | Clinical presentation | ||
---|---|---|---|---|---|---|---|
Fever ≥ 38.5 °C | Splenomegaly | Coagulopathy | |||||
1 | M | Caucasian | No | 4.9 | Yes | Yes | Yes |
2 | F | Hispanic | No | 7.0 | Yes | Yes | Yes |
3 | F | Hispanic | No | 1.0 | Yes | Yes | Yes |
4 | F | East Asian | No | 2.1 | Yes | Yes | No |
5 | M | Hispanic | No | 2.2 | Yes | Yes | No |
6 | F | Hispanic | No | 7.0 | Yes | Yes | Yes |
7 | M | East Asian | No | 4.8 | Yes | Yes | Yes |
8 | M | Caucasian | No | 19.0 | Yes | Yes | Yes |
9 | M | Hispanic | No | 15.0 | Yes | Yes | Yes |
10 | F | Hispanic | No | 1.0 | Yes | Yes | No |
11 | M | Hispanic | No | 1.0 | Yes | Yes | Yes |
12 | M | Hispanic | No | 3.0 | Yes | Yes | Yes |
13 | F | Hispanic | No | 19.0 | Yes | Yes | No |
14 | M | AA | No | 0.8 (10 months) | Yes | Yes | Yes |
15 | M | East Asian | No | 0.9 (11°months) | Yes | Yes | Yes |
*Self-identified
M male, F female, AA African American