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. 2021 Jun 26;41(7):1582–1596. doi: 10.1007/s10875-021-01073-9

Table 1.

Clinical characteristics of patients with T cell-EBV-HLH

Patient number Gender Ethnic background* Family history Age at presentation (years) Clinical presentation
Fever ≥ 38.5 °C Splenomegaly Coagulopathy
1 M Caucasian No 4.9 Yes Yes Yes
2 F Hispanic No 7.0 Yes Yes Yes
3 F Hispanic No 1.0 Yes Yes Yes
4 F East Asian No 2.1 Yes Yes No
5 M Hispanic No 2.2 Yes Yes No
6 F Hispanic No 7.0 Yes Yes Yes
7 M East Asian No 4.8 Yes Yes Yes
8 M Caucasian No 19.0 Yes Yes Yes
9 M Hispanic No 15.0 Yes Yes Yes
10 F Hispanic No 1.0 Yes Yes No
11 M Hispanic No 1.0 Yes Yes Yes
12 M Hispanic No 3.0 Yes Yes Yes
13 F Hispanic No 19.0 Yes Yes No
14 M AA No 0.8 (10 months) Yes Yes Yes
15 M East Asian No 0.9 (11°months) Yes Yes Yes

*Self-identified

M male, F female, AA African American