Table 2.
Ocular manifestations found in PXE patients (pt) in different age groups.
| Age | N. of Pt |
Pt with PO |
%/ Decade |
Pt with CO |
%/ Decade |
Pt with AS |
%/ Decade |
Pt with CL |
%/ Decade |
Pt with CNV |
%/ Decade |
Pt with PD |
%/ Decade |
Pt with PPA |
%/ Decade |
Pt with ODD |
%/ Decade |
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
| <10 | 2 | 2 | 100 | 2 | 100 | 0 | 0 | 2 | 100 | 0 | 0 | 0 | 0 | 0 | 0 | 0 | 0 |
| 20–29 | 7 | 7 | 100 | 7 | 100 | 6 | 85.7 | 5 | 71.4 | 0 | 0 | 0 | 0 | 0 | 0 | 1 | 14.3 |
| 30–39 | 11 | 11 | 100 | 11 | 100 | 10 | 90.9 | 9 | 81.8 | 2 | 18.2 | 3 | 27.3 | 1 | 9.1 | 0 | 0 |
| 40–49 | 12 | 11 | 91.7 | 11 | 91.7 | 12 | 100 | 10 | 83.3 | 5 | 41.7 | 3 | 25.0 | 1 | 8.3 | 1 | 8.3 |
| 50–59 | 11 | 10 | 90.9 | 10 | 90.9 | 11 | 100 | 7 | 63.6 | 10 | 90.9 | 8 | 72.7 | 5 | 45.5 | 1 | 9.1 |
| 60–69 | 10 | 4 | 40 | 4 | 40 | 10 | 100 | 7 | 70 | 10 | 100 | 8 | 80 | 7 | 70 | 0 | 0 |
| Sum | 53 | 45 | 45 | 49 | 40 | 27 | 22 | 14 | 3 | ||||||||
| Mean | 84.9 | 84.9 | 92.5 | 75.5 | 50.9 | 41.5 | 26.4 | 5.7 |
PO = peau d’orange; CO = coquille d’oeuf; AS = angioid streaks; CL = comet lesion; CNV = choroidal neovascularization; PD = pattern dystrophy; PPA = pole posterior atrophy; ODD = optic disk drusen.