Table 1.

A comparison of individuals with vascular Ehlers-Danlos syndrome with and without a diagnosis of aortic/arterial pathology

N (%), Median [IQR]	Aortic/Arterial pathology (n=53)	No aortic/arterial pathology (n=33)	P
Current Age	41 [31–49.5]	25 [15–41.5]	<.001
Age range	19–79	1–88	-
Age at diagnosis	32 [23–43.3]	18 [10–31]	<.001
Male	27 (50.9)	14 (42.4)	0.442
Caucasian	47 (88.7)	27 (81.8)	0.491
BMI	24.6 [21.6–27.4]	22.9 [17.1–25.3]	0.068
Hypertension	17 (32.1)	2 (6.1)	0.005
Deep vein thrombosis	12 (22.6)	1 (3)	0.014
Intestinal perforation	9 (17)	5 (15.2)	0.823
Spontaneous PTX/HTX	7 (13.2)	5 (15.2)	0.800
Current or past smoker	12 (22.6)	5 (15.2)	0.396
Family history of VEDS	24 (45.3)	18 (54.5)	0.403
Follow up post vEDS diagnosis	7.5 [3.5–12]	5 [1–11]	0.152
Died	13 (24.5)	0	0.002
Age at death	39 [27.8–51.3]	-	-