Table 1.

Summary table of poorly differentiated chordoma.

Etiology	The poorly differentiated chordoma is a rare subtype of chordoma, a primary malignancy from notochord remnants arising from bone.
Incidence	True incidence unknown. Classical chordoma accounts for approximately 4% of primary bone tumours and the poorly differentiated subtype has only been recognized in recent years.
Gender Ratio	Chordoma classical type has a slight male predominance. The poorly differentiated subtype has an unknown gender ratio.
Age Predilection	The classical skull base chordoma appears most frequently in adults (20–40 years). The poorly differentiated subtype may have a predilection for the pediatric population.
Risk factors	No known risk factors.
Treatment	Traditionally, surgical excision is first line treatment for chordoma. Some literature reports percutaneous radiofrequency ablation or external beam radiotherapy.
Prognosis	Poor. Poorly differentiated subtype of chordoma is more aggressive with a tendency to metastasize. Our patient passed away due to complications of lung metastasis.
Imaging Findings	Centered at the skull base most commonly. CT: Usually lytic and destructive lesion arising from bone, with surrounding soft tissue component. MRI: Infiltrative, non-enhancing, of uniform intermediate to low signal intensity on T1 and T2 weighted imaging.