Figure 2.

Flow chart of treatment of patients with ACM. Both healthy gene carriers and ACM patients should avoid intense sport activity, to prevent exercise-induced arrhythmic events and disease development or progression. Betablockers, since they prevent arrhythmic events and lower right ventricular wall stress, are essential drugs to be used in all clinically affected individuals. In patients suffering from VAs, AA drugs give the opportunity to improve symptoms. Catheter ablation is an interventional option for patients with episodes of sustained monomorphic VT. Patients for whom the implantation of an ICD is most often indicated are those with history of VF or sustained VT. In advanced stages of the disease, when HF occurs, betablockers and other HF drugs are indicated. AA drugs = antiarrhythmic drugs; ACM = arrhythmogenic cardiomyopathy; HF = heart failure; ICD = implantable cardioverter defibrillator; Vas = ventricular arrhythmias; VT = ventricular tachycardia; VF = ventricular fibrillation.