Table 1.
Causes of dorsal pterygium involving the nail unit
| Traumatic causes | Acute trauma: burns, penetrating injury, radiodermatitis, split nail deformity |
| Chronic trauma: onychotillomania | |
| Dermatological diseases | Lichen planus (involving the nail matrix) |
| Toxic epidermal necrolysis | |
| Porokeratosis of Mibelli | |
| Bullous diseases | Autoimmune bullous diseases: cicatricial pemphigoid, pemphigus foliaceus, pemphigus vulgaris, etc. |
| Mechanobullous diseases: epidermolysis bullosa (various variants) | |
| Bullous drug reactions with scarring | |
| Infections | Purulent infections |
| Leprosy (neuropathic damage or secondary purulent infections) | |
| Genodermatoses | Dyskeratosis congenita |
| Marfan syndrome | |
| Nail tumors | Onychomatricoma (matrix metaplasia of the ventral aspect of PNF) |
| Systemic disease | Graft versus host disease |
| Systemic lupus erythematosus | |
| Sarcoidosis (involving the PNF) | |
| Vascular causes | Raynaud's phenomenon |
| Atherosclerosis | |
| Diabetic vasculopathy | |
| Type 2 lepra reaction | |
| Idiopathic pterygium | |
PNF, proximal nail fold.