Table 1.
Data recorded in the registry in the period of the study
| Charachteristics | N (%; median; range; IQR [years of age]) |
|---|---|
| Pediatrica patients | 140 (11%; 11; 2-17; 8-14) |
| Adultb patients | 1,157 (89%;46; 18-92; 32-59) |
| Gender | N (%) |
| Males | 569 (44%) |
| Females | 728 (56%) |
| Type of C1-INH-HAE | N (%) |
| Type 1 | 1,182 (91%) |
| Type 2 | 115 (9%) |
| Age at diagnosis (n=1295) | (mean; median; range; IQR) |
| Age at diagnosis (years) | (25; 23; 0-80; 10-36) |
| No. of patients inserted attacks during the study period | |
| Patients with ≥1 attack | 497 |
| Attack inserted by the app | 359 |
| Attack inserted by a physician | 138 |
| No. of patients recorded during the study period | |
| Up to January 2018 | 440 |
| Up to January 2019 | 790 |
| Up to January 2020 | 1,129 |
a<18 years of age, b≥18 years of age, IQR = interquartile range