Table 2.

Laboratory data at diagnosis in HAE type 1 (n=1,182) and 2 (n=115)

Parameter	C1-INH-HAE type 1 (mean; median; IQR)	C1-INH-HAE type 2 (mean; median; IQR)
C4 (% of normala)	18; 15; 1–26	19; 18; 3–26
Antigenic C1-INH (% of normalb)	20; 20; 9–26	107; 108; 53–156
C1-INH function (% of normalc)	20; 17; 2–30	20; 18; 9–30

^a60 to 140%, ^b70 to 115%, ^c70 to 130%