Table 3.
gnomAD allele counts and frequency for different categories of myocilin (Refseq NM_000261.2) variants
Position | Additional variant | Allele Count | Allele Frequency | Polyphen Prediction1 | Sift prediction1 |
---|---|---|---|---|---|
Benign | |||||
p.Thr293Lys | 157 | 5.60e-04 | Benign | Tolerated | |
p.Thr293Ala | 1 | 4.02e-6 | Benign | Tolerated | |
p.Thr293Met | 3 | 1.21e-5 | Probably_damaging | Deleterious | |
p.Val329Met | 72 | 2.55e-04 | Possibly_damaging | Tolerated | |
p.Glu352Lys | 337 | 1.19e-03 | Probably_damaging | Deleterious | |
p.Thr353Ile | 191 | 6.75e-04 | Benign | Deleterious | |
p.Lys398Arg | 992 | 3.51e-03 | Benign | Tolerated | |
p.Ala445Val | 57 | 2.01e-04 | Benign | Deleterious | |
p.Lys500Arg | 161 | 5.69e-04 | Benign | Tolerated | |
p.Lys500Thr | 1 | 3.98e-6 | Benign | Tolerated | |
Pathogenic | |||||
p.Gly252Arg | N/A | N/A | |||
p.Gly252Glu | 2 | 8.25e-06 | Probably damaging | Deleterious | |
p.Gly252Ala | 3 | 1.15e-05 | Probably damaging | Deleterious | |
p.Arg272Gly | N/A | N/A | |||
p.Arg272Gln | 2 | 8.01e-06 | Benign | Tolerated | |
p.Arg272* | 2 | 8.02e-06 | High confidence loss of function | ||
p.Glu323Lys | N/A | N/A | |||
p.Glu323_Val 329dup | 1 | 3.98e-06 | |||
p.Gly364Val | N/A | N/A | |||
p.Gy364Ser | 2 | 7.95e-06 | Probably damaging | Tolerated | |
p.Pro370Leu | N/A | N/A | |||
p.Pro370Ser | 1 | 3.19e-05 | Probably damaging | Deleterious | |
p.Thr377Met | 5 | 1.99e-05 | Probably_damaging | Deleterious | |
p.Thr377Ala | 2 | 7.96e-6 | Probably_damaging | Deleterious | |
p.Pro481Thr | N/A | N/A | |||
p.Pro481Ser | 1 | 3.98e-06 | Possibly damaging | Tolerated | |
Likely Pathogenic | |||||
p.Val251Ala | N/A | N/A | |||
p.Val251Ile | 1 | 4.14e-06 | Possibly damaging | Tolerated | |
p.Leu255Pro | N/A | N/A | |||
p.Leu255Val | 3 | 1.23e-05 | Benign | Tolerated | |
p.Pro274Arg | N/A | N/A | |||
p.Pro274Leu | 1 | 4e-06 | Probably damaging | Deleterious | |
p.Thr438Ile | N/A | N/A | |||
p.Thr438Pro | 6 | 2.39e-05 | Probably damaging | Deleterious | |
p.Asn450Tyr | N/A | N/A | |||
p.Asn450Ser | 2 | 7.95e-06 | Probably damaging | Deleterious | |
Uncertain Significance—Lean Pathogenic | |||||
p.Gly244Val | 6 | 2.51e-05 | Probably_damaging | Deleterious | |
p.Gly244Arg | 2 | 7.95e-6 | Possibly_damaging | Deleterious | |
p.Thr285Met | 7 | 2.80e-05 | Probably_damaging | Deleterious | |
p.Thr285Pro | 1 | 4e-6 | Probably_damaging | Deleterious | |
p.Trp286Arg | 2 | 8.01e-06 | Probably_damaging | Deleterious | |
p.Gly300Lys | 10 | 3.58e-05 | Possibly_damaging | Tolerated | |
p.Gly326Ser | 1 | 3.98e-06 | Probably_damaging | Deleterious | |
p.Leu334Pro | 3 | 1.19e-05 | Probably_damaging | Deleterious | |
p.Leu334Val | 1 | 3.98e-6 | Probably_damaging | Deleterious | |
p.Ile360Asn | N/A | N/A | |||
p.Ile360Leu | 1 | 3.98e-06 | Benign | Tolerated | |
p.Gly387Asp | 3 | 1.19e-05 | Possibly_damaging | Deleterious | |
p.Asp395_Glu396insAspPro | N/A | N/A | |||
p.Asp395Glu | 5 | 1.99e-05 | Benign | Tolerated | |
p.Asp395Asn | 3 | 1.19e-05 | Benign | Tolerated | |
p.Gly399Asp | N/A | N/A | |||
p.Gly399Val | 4 | 1.59e-5 | Probably_damaging | Deleterious | |
p.Ser425Pro | N/A | N/A | |||
p.Ser425* | 1 | 3.98e-06 | High confidence loss of function | ||
p.Phe430Leu | N/A | N/A | |||
p.Phe430Ser | 1 | 3.98e-06 | Probably damaging | Deleterious | |
p.Arg470Cys | 6 | 3.31e-05 | Benign | Tolerated | |
p.Arg470His | 3 | 1.19e-5 | Benign | Tolerated | |
p.Arg470Leu | 1 | 3.19e-5 | Benign | Deleterious | |
Uncertain Significance—Lean Benign | |||||
p.Thr256Met | 23 | 8.36e-05 | Possibly_damaging | Tolerated | |
p.Thr256Ala | 1 | 4.11e-6 | Benign | Tolerated | |
p.Thr256Arg | 3 | 1.23e-05 | Probably damaging | Deleterious | |
p.Arg296Cys | 4 | 1.61e-5 | Probably_damaging | Deleterious | |
p.Arg296His | 17 | 6.1e-5 | Possibly_damaging | Deleterious | |
p.Arg296Leu | 1 | 4.04e-6 | Possibly_damaging | Deleterious | |
p.Gln297His | N/A | N/A | |||
p.Gln297Arg | 1 | 4.03e-06 | Benign | Tolerated | |
p.Leu303Ile | 17 | 6.08e-05 | Benign | Tolerated | |
p.Leu303Phe | 4 | 1.43e-5 | Benign | Tolerated | |
p.Ser313Phe | 17 | 6.05e-05 | Probably_damaging | Tolerated | |
p.Ser313Cys | 2 | 7.11e-6 | Probably_damaging | Deleterious | |
p.Ser331Thr | N/A | N/A | |||
p.Ser331Leu | 12 | 4.24e-05 | Benign | Tolerated | |
p.Ser333Cys | N/A | N/A | |||
p.Ser333Asn | 5 | 1.99e-05 | Possibly damaging | Deleterious | |
p.Arg342Lys | N/A | N/A | |||
p.Arg342Gly | 3 | 1.19e-05 | Benign | Deleterious | |
p.Ile345Met | N/A | N/A | |||
p.Ile345Thr | 1 | 3.98e-06 | Benign | Tolerated | |
p.Thr419Ala | 1 | 3.98e-06 | Probably_damaging | Deleterious | |
p.Arg422Cys | 8 | 3.18e-5 | Probably_damaging | Deleterious | |
p.Arg422His | 8 | 3.18e-5 | Benign | Tolerated | |
p.Ala427Thr | 12 | 4.77e-05 | Probably_damaging | Deleterious | |
p.Gly434Ser | 1 | 3.98e-06 | Possibly_damaging | Deleterious | |
p.Asp446Tyr | 8 | 2.83e-05 | Possibly_damaging | Deleterious | |
p.Asp446His | 1 | 3.98e-6 | Benign | Tolerated | |
p.Ala447Thr | N/A | N/A | |||
p.Ala447Val | 2 | 7.95e-06 | Possibly_damaging | Deleterious | |
p.Tyr471Cys | 7 | 2.78e-05 | Probably_damaging | Deleterious | |
p.Met476Arg | 3 | 1.19e-05 | Probably_damaging | Deleterious | |
p.Met476Leu | 1 | 3.98e-6 | Possibly_damaging | Deleterious | |
Uncertain Significance—Premature termination | |||||
p.Gln337Argfs*9 | N/A | N/A | |||
p.Gln337His | 1 | 3.98e-6 | Probably_damaging | Deleterious | |
p.Gln368* | 314 | 1.11e-03 | High confidence loss of function | ||
Tyr453Metsf*11 | 20 | 7.07e-5 | High confidence loss of function |
As reported within gnomAD (https://gnomad.broadinstitute.org/gene/ENSG00000034971?dataset=gnomad_r2_1)