Table 1.
Summarizes the main clinical parameters of the three patients in our study.
| Patient | Age | SCC (mEq/L) | Fecal Elastase (µg/g) | Last FEV1 (Liter, %) | Chronic Infection | CFTR-RD (Y/N) | OLTT (Y/N) |
|---|---|---|---|---|---|---|---|
| 1 * | 48 | 104 | <100 | 0.65; 26 | PA, BG | Y | Y |
| 2 * | 40 | 82 | >500 | 1.25; 38 | PA | N | Y |
| 3 | 59 | 114 | >500 | 0.59; 28 | PA | N | Y |
* These patients presented recurrent massive haemoptysis, not responding to bronchial artery embolization. Abbreviations: SCC: sweat chloride concentrations at CF diagnosis; FEV1: Forced Expiratory Volume in 1 s; CFTR-RD: CF related diabetes; PA: pseudomonas aeruginosa; BG: Burkholderia gladioli; OLTT: Oxygen Long-Term Therapy, N: Not, Y: Yes.