Table 1.

Pediatric cases of atypical antiglomerular basement membrane disease in the literature.

Publication	Age/gender	Presentation	Biopsy findings	α3NC1 antibodies	Treatment	Outcome
Jen and Auron (present case)	4/M	Nephrotic-range proteinuria, hematuria, normal renal function	One glomerulus with segmental endocapillary hypercellularity, karyorrhexis, and small cellular crescent	Positive	Rituximab, steroids, MMF	Asymptomatic with normal renal function at 15 months
Wilson and Dixon [13]	14/M	No onset of renal failure within a large cohort of typical anti-GBM disease	N/A	Positive	Steroids	Living 1 yr with normal function
	13/M			Negative	Steroids, azathioprine	Living 18 mo with normal function
	5/M			Negative	Steroids, cyclophosphamide	Living 7 yr with normal function
Nagano et al. [14]	8/F	Incidental hematuria and proteinuria on screening	Mild mesangial proliferation; no crescents	Positive	Plasmapheresis, steroids, cyclophosphamide	Decreased proteinuria and antibody titers; no long-term follow-up