Table 3.

Follow up assessment of the 37 children after long term treatment

Variables	N = 37
Follow up duration -year	2.88 ± 1.72 (0.03–9.21, median 2.83)
Age at follow up	10.63 ± 5.23 (2.45–20.04, median 11.16)
Pancreatic malfunction -no/total no (%)	15/37 (40.54)
BMI	16.87 ± 3.54
BMI centiles	32.26% ± 32.75% (0.1–98.5%, 18.9%)
BMI Z-score	−0.78 ± 1.46
Acute exacerbation times	1.62 ± 1.71
Respiratory infection times after treatment	1.97 ± 1.87
Lung function -no/total no (%)	17/37 (45.95)
FEV1	75.26% ± 22.34% (34.8–120.2%, 80%)
FVC	86.99% ± 19.95% (41.4–116.5%, 92%)
FEF75	36.63% ± 24.30% (7–99.2%, 30.3%)
Change of lung function –no/total no (%)	17/37 (45.95)
Better -no/total no (%)	7/17 (41.18)
Worse -no/total no (%)	10/17 (58.82)
Bacterial colonies -no/total no (%)	27/37 (72.97)
PA -no/total no (%)	17/27 (62.96)
SA -no/total no (%)	6/27 (22.22)
Changes of bronchiectasis -no/total no (%)	22/37 (59.46)
Decrease -no/total no (%)	3/22 (13.64)
Unchanged -no/total no (%)	13/22 (59.09)
Increase -no/total no (%)	6/22 (27.27)

Plus–minus values are means ±SD