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. Author manuscript; available in PMC: 2022 Aug 1.
Published in final edited form as: Br J Haematol. 2021 Jul 5;194(3):617–625. doi: 10.1111/bjh.17663

Table.

Characteristics of Participants.

Characteristic Median (mean; min – max) or Number (%)
Age
 Start of hydroxyurea (months) 11.8 (40.2; 6.4 – 234.6)
 Last follow-up (years) 6.0 (7.2; 2.3 – 21.9)
Sex
 Male 27 (56)
 Female 21 (44)
β-globin genotype
 βSS 46 (96)
 βS0 2 (4)
α-globin genotype
 αα/αα 30 (63)
 αα/–α 12 (25)
 −α/–α 4 (8)
 αα/ααα 2 (4)