Table 1.
Different phenotypes and characters of Kawasaki disease.
| Phenotypes | Kawasaki disease (KD) | KD shock syndrome (KDSS) | |
|---|---|---|---|
| Typical KD | Atypical KD | ||
| Criteria | ≧4/5 | <4/5 | ≧4/5 + shock |
| Myocarditis | 5% | 20% | 20% |
| Age (year) (avg) | 0.5–5.0 (2.0) | Frequent <0.5 or >5 | 2–12 (3.5) |
| Platelets (1,000/ul) | >350 | >450 | High or low |
| WBC (/mm3) | >10,000 | >15,000 | Variable |
| Pyuria | Some | Frequent | Frequent |
| CRP (mg/dl) | 3–15 | >3 | >10 |
| Procalcitonin (ng/ml) | >0.5 | Variable | >1.0 |
| Ferritin (ng/ml) | 100–200 | 100–200 | >500 |
| Coagulopathy | No | Some | Often |
| D-dimer (ng/ml) | <1,000 | <1,000 | >1,000 |
| Cytokines | IL-6, IL-10, IP-10 | IL-6 | IL-6, INF-γ, IL-10 |
| IVIG Resistance (%) | 15 | >15 (delayed Rx) | 40 |
| Fatality (%) | 0.1 | Unknown | 2 |
WBC, white blood cell; CRP, C-reaction protein; IL, interleukin; INF, interferon; IP, interferon-γ induced protein; IVIG, intravenous immunoglobulin.