Table 1.
Annual incidence and median age at diagnosis for each type of cardiomyopathy (CM).
| Type of CM | Age range at diagnosis | Number of cases | Median age at diagnosis | Annual incidence per 100,000 children | References | ||
|---|---|---|---|---|---|---|---|
| All cases | Age at diagnosis <1 y | All cases | Age at diagnosis <1 y | ||||
| DCM | 0–18 y | 239 | – | 1.8 y | 0.58 | 4.58 | PCMR (7) |
| 0–10 y | 184 | 121 | 7.5 m | 0.73 | 4.76 | NACCS (17) | |
| 0–20 y | 56 | 29 | 1.1 y | 0.34 | 3.8 | Finland study (18) | |
| HCM | 0–18 y | 196 | – | 5.9 y | 0.47 | 3.2 | PCMR (7) |
| 0–10 y | 80 | 48 | 5.7 m | 0.32 | 1.89 | NACCS (17) | |
| 0–20 y | 40 | 2 | 13 y | 0.24 | 0.26 | Finland study (18) | |
| RCM | 0–10 y | 8 | 0 | 3 y | 0.03 | 0 | NACCS (17) |
| 0–20 y | 6 | 0 | 7.2 y | – | 0 | Finland study (18) | |
| Othera | 0–18 y | 15 | – | – | 0.04 | – | PCMR (7) |
| Unclassifiedb | 0–10 y | 42 | 30 | 3.8 m | 0.17 | 1.18 | NACCS (17) |
| Total | 0–18 y | 467 | 193 | – | 1.13 | 8.34 | PCMR (7) |
| 0–10 y | 314 | 199 | – | 1.24 | 7.84 | NACCS (17) | |
| 0–20 y | 107 | 31 | – | 0.65 | 4.1 | Finland study (18) | |
a
Includes restrictive and other identified types of CM.
b
Includes LVNC (29 of 42 cases).